Prophyria 

prophyrin build up in the body 

Acute abdomen without signs and psychiatric symptoms --> think of prophyria

3 keys 

• high carbohydrate infusion 

• IV hemin

• Avoid prophyrogenic drugs 

Prophyria cutanea larta 

characteristic photosensitive rash on sun exposed area : hand, face, legs

liver - accumulates prophyria - carcinogenic 

Treatment 

- avoid sun exposure 

- avoid iron containing food 

- stopped hormone replacement therapy

- stop alcohol

Erythropoietic Prophyria

• common amongst boys around 5 yr old 

• rash after minutes of sun exposure - 

Treatment - avoid sun exposure 

cholestyramine