-AV & VA discordance
-might at usual or inverted atrial arrangement
-major assoc xx
-VSD (>75% pts)
-valvar or subvalvar PS (LVOTO- but remember LV is on R side/pulm side) - LVOTO in >50% pts
-TV malformations (TV on L side/systemic side) --> systemic AV vlv regurg
-abNl coronary arts
-abNl conduction system - anterior AV nd/His bundle, complete HB (congen or post op)
-GA xx- Ao often ant/left of PA, nearlly side/side, but variable
Nomenclature
-ccTGA
-discordant transposition
-AV & VA discordance
-physiologically corrected transposition
-double discordance
-AV discordance w transposition
-L-transposition
-Inverted transposition
-mixed levocardia/mixed dextrocardia
-dextroversion
-SLL = situs solitus, L looped, L transposed GAs
-or IDD - situs inversus, D looped, D transposed GAs
Anatomy
-usually atrial situs solitus w LV on R and RV on L, but w LV slightly post and inf to RV
-mirror image if atrial situs inversus
-AV vlvs stay w their ventricle
-malposition of hrt common
-apex usually leftward, and formed by RV
-1/4 pts have dextrocardia, some w mesocardia
-dextrocardia- assoc w dextrorotation of hrt, so RA is more posterior
-mirror image if atrial inversus