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3. Shakkottai VG, Sudha R, Balaram P. Gramicidin S: A peptide model for protein glycation and reversal of glycation using nucleophilic amines. J Pept Res. 2002;60:112-120.
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13. do Carmo Costa M, Luna-Cancalon K, Fischer S, Ashraf NS, Ouyang M, Dharia RM, Martin-Fishman L, Yang Y, Shakkottai VG, Davidson BL, Rodríguez-Lebrón E, Paulson HL. Toward RNAi therapy for the polyglutamine disease Machado-Joseph disease. Mol Ther. 2013;21:1898-1908.
14. Ashizawa T, Figueroa KP, Perlman S, Gomez, CM, Wilmot G, Schmahmann J, Ying S, Zesiewicz T, Paulson H, Shakkottai V, Bushara K, Kuo S, Geschwind M, , Xia G, Mazzoni P, Krischer J, Cuthbertson D, Holbert A, Ferguson J, Pulst S Subramony SH. Clinical characteristics of patients with spinocerebellar ataxias 1, 2, 3 and 6 in the US; prospective observational study. Orphanet J Rare Dis. 2013 Nov 13;8:177.
15. Luna-Cancalon K, Sikora KM, Pappas SS, Singh V, Wulff H, Paulson HL, Burmeister M, Shakkottai VG. Alterations in cerebellar physiology are associated with a stiff-legged gait in Atcayji-hes mice. Neurobiol Dis. 2014 Jul;67:140-8.
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17. Lo R, Figueroa KP, Pulst S, Lin C-Y, Perlman S, Wilmot G, Gomez C, Schmahmann J, Paulson H, Shakkottai VG, Ying S, Zesiewicz T, Bushara K, Geschwind M, Xia G, Subramony SH, Ashizawa T, Kuo S-H. Coenzyme Q10 and Spinocerebellar Ataxias. Movement Disorders. 2015 Feb;30(2):214-20.
18. Lo R, Figueroa KP, Pulst S, Lin C-Y, Perlman S, Wilmot G, Gomez C, Schmahmann J, Paulson H, Shakkottai VG, Ying S, Zesiewicz T, Bushara K, Geschwind M, Xia G, Subramony SH, Ashizawa T, Kuo S-H. Vascular Risk Factors and Clinical Progression in Spinocerebellar Ataxias. Tremor Other Hyperkinet Mov (NY). 2015 Feb 2;5:287.
19. Moscovich M, Okun M, Favilla C, Figueroa K, Pulst S, Perlman S, Wilmot G, Gomez C, Schmahmann J, , Paulson H, Shakkottai V, Ying S, Zesiewicz T, Kuo S-H, Bushara K Beaulieu R, Xia G, Beaulieu B, Ashizawa T, Subramony S. Clinical Evaluation of Eye Movements in Spinocerebellar Ataxias- A Prospective Multicenter Study. J Neuroophthalmol. 2015 Mar;35(1):16-21.
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Highlighted in Nature Reviews Neuroscience. Published online: 03 September 2015